Difference between revisions of "혈우병"

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2. 응고 인자의 종류는 여러 가지가 있으나, 영향을 미치는 것은 크게 3가지로 구분되며, 이것이 혈우병 타입을 결정한다.<br />
 
2. 응고 인자의 종류는 여러 가지가 있으나, 영향을 미치는 것은 크게 3가지로 구분되며, 이것이 혈우병 타입을 결정한다.<br />
 
&nbsp;&nbsp; * 혈우병 타입:<br />
 
&nbsp;&nbsp; * 혈우병 타입:<br />
&nbsp;&nbsp;&nbsp; <a title="Haemophilia A" href="http://en.wikipedia.org/wiki/Haemophilia_A" moz-do-not-send="true">- Haemophilia A</a> involves a lack of the clotting <a title="Factor VIII" href="http://en.wikipedia.org/wiki/Factor_VIII" moz-do-not-send="true">Factor VIII</a>. (This represents 90% of haemophilia cases.<sup class="noprint Template-Fact"><span title="This claim needs references to reliable sources since October 2007" style="WHITE-SPACE: nowrap">[<em><a title="Wikipedia:Citation needed" href="http://en.wikipedia.org/wiki/Wikipedia:Citation_needed" moz-do-not-send="true">citation needed</a></em>]</span></sup>)<br />
+
&nbsp;&nbsp;&nbsp; - Haemophilia A involves a lack of the clotting Factor VIII. (This represents 90% of haemophilia cases.<sup class="noprint Template-Fact"><span title="This claim needs references to reliable sources since October 2007" style="WHITE-SPACE: nowrap">[<em>citation needed</em>]</span></sup>)<br />
&nbsp;&nbsp;&nbsp; - <a title="Haemophilia B" href="http://en.wikipedia.org/wiki/Haemophilia_B" moz-do-not-send="true">Haemophilia B</a> involves a lack of the clotting <a title="Factor IX" href="http://en.wikipedia.org/wiki/Factor_IX" moz-do-not-send="true">Factor IX</a>.<br />
+
&nbsp;&nbsp;&nbsp; - Haemophilia B involves a lack of the clotting Factor IX.<br />
&nbsp;&nbsp;&nbsp; <a title="Haemophilia C" href="http://en.wikipedia.org/wiki/Haemophilia_C" moz-do-not-send="true">- Haemophilia C</a> involves a lack of the clotting <a title="Factor XI" href="http://en.wikipedia.org/wiki/Factor_XI" moz-do-not-send="true">Factor XI</a>.3. <a title="Haemophilia A" href="http://en.wikipedia.org/wiki/Haemophilia_A" moz-do-not-send="true">Haemophilia A</a> (데이터베이스: <span lang="EN-US" style="FONT-SIZE: 12pt; FONT-FAMILY: 굴림"><a href="http://europium.csc.mrc.ac.uk/WebPages/Main/main.htm" moz-do-not-send="true">http://europium.csc.mrc.ac.uk/WebPages/Main/main.htm</a>)<br />
+
&nbsp;&nbsp;&nbsp; - Haemophilia C involves a lack of the clotting Factor XI.3. Haemophilia A&nbsp;<br />
4. Haemophila B (DB: &nbsp; <a class="moz-txt-link-freetext" href="http://www.kcl.ac.uk/ip/petergreen/haemBdatabase.html" moz-do-not-send="true">http://www.kcl.ac.uk/ip/petergreen/haemBdatabase.html</a>)<br />
+
&nbsp;&nbsp;&nbsp;&nbsp;&nbsp; (데이터베이스: <span lang="EN-US" style="FONT-SIZE: 12pt; FONT-FAMILY: 굴림"><a moz-do-not-send="true" href="http://europium.csc.mrc.ac.uk/WebPages/Main/main.htm">http://europium.csc.mrc.ac.uk/WebPages/Main/main.htm</a>)<br />
 +
4. Haemophila B (DB: &nbsp; <a class="moz-txt-link-freetext" moz-do-not-send="true" href="http://www.kcl.ac.uk/ip/petergreen/haemBdatabase.html">http://www.kcl.ac.uk/ip/petergreen/haemBdatabase.html</a>)<br />
 
5. Haemophila C (DB: Unknown)</span></p>
 
5. Haemophila C (DB: Unknown)</span></p>

Latest revision as of 22:09, 26 November 2007

혈우병 (Hemophilia)

  • 혈액 응고에 필요한 요인 중 하나가 결핍된 일련의 유전적 출혈장애
  • A형 혈우병(classic hemophilia) - 항혈우병 제 8인자가 결핍된 결과
  • B형 혈우병(Chrismas disease) - 혈장 트롬보플라스틴 요소의 결핍으로 인함.


1. 혈우병은 혈액 응고 인자의 부족으로 생기고,
2. 응고 인자의 종류는 여러 가지가 있으나, 영향을 미치는 것은 크게 3가지로 구분되며, 이것이 혈우병 타입을 결정한다.
   * 혈우병 타입:
    - Haemophilia A involves a lack of the clotting Factor VIII. (This represents 90% of haemophilia cases.[citation needed])
    - Haemophilia B involves a lack of the clotting Factor IX.
    - Haemophilia C involves a lack of the clotting Factor XI.3. Haemophilia A 
      (데이터베이스: http://europium.csc.mrc.ac.uk/WebPages/Main/main.htm)
4. Haemophila B (DB:   http://www.kcl.ac.uk/ip/petergreen/haemBdatabase.html)
5. Haemophila C (DB: Unknown)